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KMID : 0356920090570030371
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Korean Journal of Anesthesiology
2009 Volume.57 No. 3 p.371 ~ p.375
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Anesthetic managements for correction of aortic valve regurgitation in a patient with Loeys-Dietz Syndrome - A case report -
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Kim Seong-Hyop
Kim Tae-Yop
Kwon Won-Kyoung
Kim Duk-Kyung
Woo Nam-Sik
Lim Jeong-Ae
Yoon Tae-Gyoon
Baek Seung-Woo
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Abstract
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Loeys-Dietz Syndrome (LDS) is a recently described autosomal dominant aortic aneurysm syndrome with widespread systemic involvement. It is characterized by the triad of 1) arterial tortuosity and aneurysms, 2) hypertelorism, and 3) bifid uvula or cleft palate. A 12-year-old boy with LDS was scheduled to undergo correction of aortic valve regurgitation due to aortic annuloectasia. We report our clinical experiences of a case of LDS patient with brief review of related literatures and relevant anesthetic problems.
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KEYWORD
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Anesthetic managements, Aortic valve regurgitation, Loeys-Dietz Syndrome
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